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VOLUME 7 , ISSUE 1 ( January-June, 2022 ) > List of Articles


Anesthetic Management of a Rare Case of Uterine Leiomyoma with Intravenous and Intracardiac Leiomyomatosis

Abhishek P Singh, Shilpa S Bhojraj, Nitin M Bhorkar, Anam Penkar

Keywords : Anesthesia, Cardiopulmonary bypass, Deep hypothermic circulatory arrest, Intracardiac leiomyomatosis, Intravenous leiomyomatosis

Citation Information : Singh AP, Bhojraj SS, Bhorkar NM, Penkar A. Anesthetic Management of a Rare Case of Uterine Leiomyoma with Intravenous and Intracardiac Leiomyomatosis. Res Inno Anesth 2022; 7 (1):29-31.

DOI: 10.5005/jp-journals-10049-2008

License: CC BY-NC 4.0

Published Online: 30-03-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Background: Intravenous leiomyomatosis (IVL) is an uncommon entity characterized by the growth of benign, smooth muscle tumors within the venous system. Intracardiac extension of this tumor is rare, and very few cases have been reported in the literature. Case description: We describe a case of IVL with intracardiac extension in a 55-year-old woman, who presented with severe dyspnea, ascites, and lower limb edema. Two-dimensional transthoracic echocardiography and computed tomography showed that the pelvic mass infiltrated the inferior vena cava via the iliac vessels and was extending to the right ventricle and pulmonary artery. The patient underwent a one-stage multidisciplinary thoracoabdominal operation with cardiopulmonary-bypass and deep hypothermic circulatory arrest. Conclusion: Due to the rarity of the present pathology, awareness is widely scarce and diagnosis is often deferred. A correct timely diagnosis, reasonable perioperative plan, and radical excision guarantees favorable outcomes.

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