Journal of Research & Innovation in Anesthesia

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VOLUME 4 , ISSUE 1 ( January-June, 2019 ) > List of Articles

CASE REPORT

Anesthetic Management of a Patient with Coffin–Siris Syndrome

Deepa Divakar, Pravin Virappa Ubale, Pinakin Gujjar

Keywords : Coarse facial features, Coffin–Siris syndrome, Difficult airway

Citation Information : Divakar D, Ubale PV, Gujjar P. Anesthetic Management of a Patient with Coffin–Siris Syndrome. Res Inno in Anesth 2019; 4 (1):16-18.

DOI: 10.5005/jp-journals-10049-0061

License: CC BY-NC 4.0

Published Online: 01-06-2019

Copyright Statement:  Copyright © 2019; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Coffin–Siris syndrome (CSS) is a rare genetic condition with characteristic musculoskeletal abnormalities and growth restrictions, coarse facial features, feeding abnormalities, systemic malformation, and developmental and cognitive delay.1–3 Main anesthetic concerns should be difficult airway that tends to get worse with age, risk of aspiration, and periop pulmonary complications in uncooperative and mentally retarded patients. We report a case of 9-years-old male patient with CSS for dental extraction and restoration under general anesthesia.


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